Treatment of Chylothorax with Pleurodesis, a Lesser Known Complication of Behçet's Disease: A Case Report

  • Ertan Demirdaş Department of Cardiovascular Surgery, Faculty of Medicine, Bozok University, Yozgat, Turkey.
  • Kıvanç Atılgan Department of Cardiovascular Surgery, Faculty of Medicine, Bozok University, Yozgat, Turkey.
  • Cengiz Zafer Er Department of Cardiovascular Surgery, Faculty of Medicine, Bozok University, Yozgat, Turkey.
  • Süleyman Emre Akın Yozgat State Hospital, Yozgat, Turkey.
Keywords: Chylothorax, Behcet syndrome, Vasculitis, Thrombosis

Abstract

Behçet's Disease (BD) is a multisystemic vasculitis which usually affects optical, genital, and oral mucosae and often reoccurs intermittently. Chylothorax is a very rare complication of BD which usually causes thrombosis in the major venous system. A 27-year-old man with a 10-year history of BD referred to our cardiovascular surgery department with symptoms of serious aches in the left arm, edema, and apparent veins on the left anterior chest wall. A total thrombosis of the left internal and external jugular veins and the left subclavian vein was observed. One month after a successful treatment and discharge, the patient returned to our clinic with symptoms of dyspnea and coughs. A chest radiograph showed a consolidated region. A milky liquid was aspirated through thoracocentesis from the left thorax, and its biochemical analysis helped us arrive at a diagnosis of chylothorax. The patient was hospitalized and administered corticosteroids and immunosuppressive therapy with a high-carbohydrate and low-fat dietary regimen for BD. Thereafter, a left thoracic drainage system was established. On the seventh day of hospitalization, due to a progressing cheilosis flow, a pleurodesis process was applied with talcum powder. However, the chylous drainage was continued and 60 mL of venous autologous blood was injected into the left thorax through a drainage tube. The treatment was successful, and the patient was discharged from the hospital uneventfully. At 1 month’s follow-up, the chest radiograph was normal.

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Published
2018-10-15
How to Cite
1.
Demirdaş E, Atılgan K, Er C, Akın S. Treatment of Chylothorax with Pleurodesis, a Lesser Known Complication of Behçet’s Disease: A Case Report. jthc. 13(4):180-2.
Section
Case Report(s)