Coarctation Balloon Angioplasty in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and Ebstein's Anomaly
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Abstract
The concurrent presence of coarctation of the aorta, Ebstein's anomaly, and transposition of the great arteries is extremely rare. We report a unique case of complex congenital heart disease presenting with respiratory distress and cyanosis at birth. Echocardiography revealed congenitally corrected transposition of the great arteries (ccTGA), Ebstein's tricuspid anomaly, moderate to severe tricuspid regurgitation (TR), a small muscular ventricular septal defect (VSD) and an abnormal left arch with severe coarctation of the aorta (CoA). Because of unstable hemodynamic status, balloon angioplasty was performed for the patient. Long-term clinical follow-up confirmed the effectiveness of this intervention.
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4. He BJ, Merriman AF, Cakulev I, Stambler BS, Srivastava D, Scheinman MM. Ebstein’s Anomaly: Review of Arrhythmia Types and Morphogenesis of the Anomaly. Clinical Electrophysiology. 2021;7(9):1198-206.
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7. Kuehl KS, Loffredo CA. Population‐based study of l‐transposition of the great arteries: possible associations with environmental factors. Birth Defects Research Part A: Clinical and Molecular Teratology. 2003;67(3):162-7.
8. Khajali Z, Maleki M, Mohebbi B, Aliramezany M. Coarctation stenting in a rare case with congenitally corrected transposition of the great arteries and the bicuspid aortic valve. The Journal of Tehran University Heart Center. 2020;15(1):27.
9. Mishra AK, Barwad P, Bansal V, Mandal B, Srivastava A, Naganur SH. Ebstein's anomaly of tricuspid valve with aortic stenosis and coarctation of aorta: Successful single‐stage repair of a rare adult congenital heart disease. Journal of Cardiac Surgery. 2020;35(11):3160-5.
10. Ojha V, Singh SP, Ponnuswamy KG, Jagia P. Transposition of great arteries with coarctation of aorta: a rare association demonstrated on dual source CT. Acta Cardiologica. 2021;76(2):214-5.
11. Ylinen MK, Tyni VE, Pihkala JI, Salminen JT, Sairanen H, Sarkola T. Procedural risk factors, incidence and timing of reintervention after treatment for native coarctation of the aorta in children: a population-based study. European Journal of Cardio-Thoracic Surgery. 2019;55(3):564-71.
12. Sendzikaite S, Sudikiene R, Lubaua I, Silis P, Rybak A, Brzezinska-Rajszys G, et al. Multi-centre cross-sectional study on vascular remodelling in children following successful coarctation correction. Journal of Human Hypertension. 2021:1-7.
2. Bakhshaliyev S, Özalp ZGK, Güneş M, Genç SB, Kamalı H, Şengül FS, et al. Surgical treatment of Ebstein anomaly in pediatric patients: a 10‐year single‐center study. Journal of Cardiac Surgery. 2021;36(9):3138-45.
3. Walsh EP. Ebstein’s anomaly of the tricuspid valve: a natural laboratory for re-entrant tachycardias. JACC: Clinical Electrophysiology. 2018;4(10):1271-88.
4. He BJ, Merriman AF, Cakulev I, Stambler BS, Srivastava D, Scheinman MM. Ebstein’s Anomaly: Review of Arrhythmia Types and Morphogenesis of the Anomaly. Clinical Electrophysiology. 2021;7(9):1198-206.
5. Doshi AR, Chikkabyrappa S. Coarctation of aorta in children. Cureus. 2018;10(12).
6. Ganigara M, Doshi A, Naimi I, Mahadevaiah GP, Buddhe S, Chikkabyrappa SM, editors. Preoperative physiology, imaging, and management of coarctation of aorta in children. Seminars in cardiothoracic and vascular anesthesia; 2019: SAGE Publications Sage CA: Los Angeles, CA.
7. Kuehl KS, Loffredo CA. Population‐based study of l‐transposition of the great arteries: possible associations with environmental factors. Birth Defects Research Part A: Clinical and Molecular Teratology. 2003;67(3):162-7.
8. Khajali Z, Maleki M, Mohebbi B, Aliramezany M. Coarctation stenting in a rare case with congenitally corrected transposition of the great arteries and the bicuspid aortic valve. The Journal of Tehran University Heart Center. 2020;15(1):27.
9. Mishra AK, Barwad P, Bansal V, Mandal B, Srivastava A, Naganur SH. Ebstein's anomaly of tricuspid valve with aortic stenosis and coarctation of aorta: Successful single‐stage repair of a rare adult congenital heart disease. Journal of Cardiac Surgery. 2020;35(11):3160-5.
10. Ojha V, Singh SP, Ponnuswamy KG, Jagia P. Transposition of great arteries with coarctation of aorta: a rare association demonstrated on dual source CT. Acta Cardiologica. 2021;76(2):214-5.
11. Ylinen MK, Tyni VE, Pihkala JI, Salminen JT, Sairanen H, Sarkola T. Procedural risk factors, incidence and timing of reintervention after treatment for native coarctation of the aorta in children: a population-based study. European Journal of Cardio-Thoracic Surgery. 2019;55(3):564-71.
12. Sendzikaite S, Sudikiene R, Lubaua I, Silis P, Rybak A, Brzezinska-Rajszys G, et al. Multi-centre cross-sectional study on vascular remodelling in children following successful coarctation correction. Journal of Human Hypertension. 2021:1-7.
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| Issue | Articles In Press | |
| Section | Case Report(s) | |
| Keywords | ||
| Coarctation of the aorta; Transposition of great arteries; Ebstein's anomaly | ||
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How to Cite
1.
Alipour A, Alizadeh B, Zargaran B. Coarctation Balloon Angioplasty in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and Ebstein’s Anomaly. J Tehran Heart Cent. 2024;.
