Coarctation Balloon Angioplasty in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and Ebstein’s Anomaly
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Abstract
The coexistence of aortic coarctation, Ebstein’s anomaly, and transposition of the great arteries is an extremely rare occurrence. In this case report, we present a unique instance of complex congenital heart disease in a neonate who exhibited respiratory distress and cyanosis at birth. Echocardiography revealed several significant findings: congenitally corrected transposition of the great arteries, Ebstein’s tricuspid anomaly, moderate-to-severe tricuspid regurgitation, a small muscular ventricular septal defect, and an abnormal left arch with severe coarctation of the aorta. Due to the patient’s unstable hemodynamic status, balloon angioplasty was performed. Subsequent long-term clinical follow-up confirmed the efficacy of this intervention.
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9. Mishra AK, Barwad P, Bansal V, Mandal B, Srivastava A, Naganur SH. Ebstein's anomaly of tricuspid valve with aortic stenosis and coarctation of aorta: Successful single-stage repair of a rare adult congenital heart disease. J Card Surg 2020;35:3160-3165.
10. Ojha V, Singh SP, Ponnuswamy KG, Jagia P. Transposition of great arteries with coarctation of aorta: a rare association demonstrated on dual source CT. Acta Cardiol 2021;76:214-215.
11. Ylinen MK, Tyni VE, Pihkala JI, Salminen JT, Sairanen H, Sarkola T. Procedural risk factors, incidence and timing of reintervention after treatment for native coarctation of the aorta in children: a population-based study†. Eur J Cardiothorac Surg 2019;55:564-571.
12. Sendzikaite S, Sudikiene R, Lubaua I, Silis P, Rybak A, Brzezinska-Rajszys G, Obrycki Ł, Jankauskiene A, Litwin M. Multi-centre cross-sectional study on vascular remodelling in children following successful coarctation correction. J Hum Hypertens 2022;36:819-825.
2. Bakhshaliyev S, Özalp ZGK, Güneş M, Genç SB, Kamalı H, Şengül FS, Ergün S, Haydin S. Surgical treatment of Ebstein anomaly in pediatric patients: A 10-year single-center study. J Card Surg 2021;36:3138-3145.
3. Walsh EP. Ebstein's Anomaly of the Tricuspid Valve: A Natural Laboratory for Re-Entrant Tachycardias. JACC Clin Electrophysiol 2018;4:1271-1288.
4. He BJ, Merriman AF, Cakulev I, Stambler BS, Srivastava D, Scheinman MM. Ebstein's Anomaly: Review of Arrhythmia Types and Morphogenesis of the Anomaly. JACC Clin Electrophysiol 2021;7:1198-1206.
5. Doshi AR, Chikkabyrappa S. Coarctation of Aorta in Children. Cureus 2018;10:e3690.
6. Ganigara M, Doshi A, Naimi I, Mahadevaiah GP, Buddhe S, Chikkabyrappa SM. Preoperative Physiology, Imaging, and Management of Coarctation of Aorta in Children. Semin Cardiothorac Vasc Anesth 2019;23:379-386.
7. Kuehl KS, Loffredo CA. Population-based study of l-transposition of the great arteries: possible associations with environmental factors. Birth Defects Res A Clin Mol Teratol 2003;67:162-167.
8. Khajali Z, Maleki M, Mohebbi B, Aliramezany M. Coarctation Stenting in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and the Bicuspid Aortic Valve. J Tehran Heart Cent 2020;15:27-30.
9. Mishra AK, Barwad P, Bansal V, Mandal B, Srivastava A, Naganur SH. Ebstein's anomaly of tricuspid valve with aortic stenosis and coarctation of aorta: Successful single-stage repair of a rare adult congenital heart disease. J Card Surg 2020;35:3160-3165.
10. Ojha V, Singh SP, Ponnuswamy KG, Jagia P. Transposition of great arteries with coarctation of aorta: a rare association demonstrated on dual source CT. Acta Cardiol 2021;76:214-215.
11. Ylinen MK, Tyni VE, Pihkala JI, Salminen JT, Sairanen H, Sarkola T. Procedural risk factors, incidence and timing of reintervention after treatment for native coarctation of the aorta in children: a population-based study†. Eur J Cardiothorac Surg 2019;55:564-571.
12. Sendzikaite S, Sudikiene R, Lubaua I, Silis P, Rybak A, Brzezinska-Rajszys G, Obrycki Ł, Jankauskiene A, Litwin M. Multi-centre cross-sectional study on vascular remodelling in children following successful coarctation correction. J Hum Hypertens 2022;36:819-825.
| Files | ||
| Issue | Vol 19 No 2 (2024): J Teh Univ Heart Ctr | |
| Section | Case Report(s) | |
| DOI | https://doi.org/10.18502/jthc.v19i2.16203 | |
| Keywords | ||
| Coarctation of the aorta Transposition of great arteries Ebstein’s anomaly Angioplasty Percutaneous transluminal angioplasty (PTA) | ||
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This work is licensed under a Creative Commons Attribution-NonCommercial 4.0 International License. |
How to Cite
1.
Alipour A, Alizadeh B, Zargaran B. Coarctation Balloon Angioplasty in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and Ebstein’s Anomaly. J Tehran Heart Cent. 2024;19(2):132-135.
