Case Report

A Case of Coronary Cameral Fistula: When and How to Intervene?


Coronary artery fistulas constitute a rare anomaly defined as an abnormal communication between a coronary artery and a great vessel or any cardiac chamber. The majority of these fistulas arise from the right coronary artery and the left anterior descending coronary artery; the circumflex coronary artery is rarely involved.  We present an unusual case of a coronary artery fistula in a middle-aged woman who presented with symptoms of heart failure and abnormal auscultation. Echocardiography and conventional and computed tomography angiography showed that the coronary fistula originated from the left circumflex coronary artery and drained majorly into the right ventricle. Given the complex anatomy of the fistula, we managed it surgically rather than percutaneously. There were no complications early after surgery and at 1 year’s follow-up.

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IssueVol 15 No 4 (2020): J Teh Univ Heart Ctr QRcode
SectionCase Report(s)
Heart Defects; Congenital Fistula Computed tomography angiography

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How to Cite
Peighambari M, Pakbaz M, Alizadehasl A, Hosseini S, Pouraliakbar H. A Case of Coronary Cameral Fistula: When and How to Intervene?. J Tehran Heart Cent. 15(4):189-194.