Coarctation Stenting in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and the Bicuspid Aortic Valve

A rare association of CCTGA

  • Zahra Khajali Department of Cardiovascular Medicine, Shaheed Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
  • Majid Maleki Department of Cardiovascular Medicine, Shaheed Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
  • Bahram Mohebbi Department of Cardiovascular Medicine, Shaheed Rajaei Cardiovascular Medical and Research Center, Iran University of Medical Sciences, Tehran, Iran.
  • Maryam Aliramezany Mail Cardiovascular Research Center, Institute of Basic and Clinical Physiology Sciences, Kerman University of Medical Sciences, Kerman, Iran.
Keywords:
Transposition of great vessels coarctation, Bicuspid aortic valve, Aortic coarctation, Surgical procedures; operative

Abstract

Congenitally corrected transposition of the great arteries (cc-TGA) is a rare congenital abnormality that occurs in 1 per 33000 live births. This abnormality comprises nearly 0.05% of all congenital heart defects, with at least 90% of cc-TGA patients having associated cardiac defects; some of these associated defects are, however, very rare. In this case report, we describe a 22-year-old man who referred to our hospital for the evaluation of hypertension and cardiac murmurs. Via echocardiography and catheterization, the patient was finally diagnosed with cc-TGA, bicuspid aortic valve, and coarctation of the aorta. He underwent successful percutaneous transarterial coarctoplasty without any complications at early and 6 months’ follow-up visits.

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Published
2020-01-29
How to Cite
1.
Khajali Z, Maleki M, Mohebbi B, Aliramezany M. Coarctation Stenting in a Rare Case with Congenitally Corrected Transposition of the Great Arteries and the Bicuspid Aortic Valve. J Tehran Heart Cent. 15(1):27-30.
Section
Case Report(s)